Development and In Vitro Characterization of [H]GMC-058 as Radioligand for Imaging Parkinsonian-Related Proteinopathies.

Publication date: Jun 09, 2025

The molecular imaging of α-synuclein (α-syn) pathology in Parkinson’s disease (PD) and related movement disorders is a clinically unmet need. The aim of this study was to discover and characterize in vitro a radioligand for imaging α-syn pathology. A library of 78 small molecules was developed and screened using recombinant α-syn fibrils and brain homogenates from Alzheimer’s disease (AD) donors. The selection criteria were as follows: Ki < 30 nM, Ki and Ki > 200 nM. Three compounds, GMC-073 (K: 8 nM), GMC-098 (Ki: 9. 7 nM), and GMC-058 (Ki: 22. 5 nM), fulfilled the criteria and were radiolabeled with H. [H]GMC-058 was the only compound with negligible binding in controls, and was further evaluated using tissue microarrays, autoradiography on fresh-frozen brain slices, and in vitro saturation binding assay on brain homogenates. [H]GMC-058 binding co-localized with α-syn inclusions in Parkinson’s disease (PD) and multiple-system atrophy (MSA), with dense A-β plaques in cerebral amyloid angiopathy and AD and with p-tau inclusions in progressive supranuclear palsy (PSP) and corticobasal degeneration (CBD). Specific binding was highest in PSP and CBD. In vitro K was highest in AD (5. 4 nM), followed by PSP (41 nM) and CBD (75 nM). The K in MSA, PD, and controls was >100 nM. [H]GMC-058 is a novel radioligand displaying a low affinity for aggregated α-syn in tissue, with an in vitro profile also suitable for detecting tau pathology in 4R tauopathies.

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Concepts Keywords
Angiopathy Aged
Negligible alpha-Synuclein
Parkinsonian alpha-Synuclein
Proteinopathies Alzheimer Disease
Autoradiography
Brain
Female
Humans
in vitro assay
Lewy bodies
Ligands
Ligands
Male
neurodegeneration
Parkinson Disease
proteinopathy
Radiopharmaceuticals
Radiopharmaceuticals

Semantics

Type Source Name
disease MESH Proteinopathies
disease MESH Parkinson’s disease
disease MESH movement disorders
disease MESH Alzheimer’s disease
disease MESH atrophy
disease MESH cerebral amyloid angiopathy
disease MESH progressive supranuclear palsy
disease MESH corticobasal degeneration
drug DRUGBANK Cannabidiol
disease MESH tauopathies
pathway KEGG Alzheimer disease
pathway KEGG Parkinson disease

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