Huntington’s Disease
Huntington’s disease, also known as Huntington’s chorea, is a hereditary neurodegenerative disorder that affects both the brain and the body. It is named after Dr. George Huntington, who first described the condition in the late 19th century.
Huntington’s disease is caused by a genetic mutation in the huntingtin gene (HTT), which leads to the production of abnormal huntingtin protein. The mutation involves an abnormal repetition of the CAG trinucleotide within the gene, causing an expansion of the repeating sequence. The more repeats a person has, the earlier and more severe the onset of the disease tends to be.
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Publication date: Dec 05, 2024 There is a growing consensus that brain development in Huntington’s ...
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Therapeutic targeting of the oxidative stress generated by pathological molecular pathways in the neurodegenerative diseases, ALS and Huntington’s.
Publication date: Dec 05, 2024 Neurodegenerative disorders are characterized by a progressive decline of specific ... -
No Evidence of Early Developmental Delay in Juvenile-Onset Huntington’s Disease Patients.
Publication date: Dec 07, 2024 Previous studies suggest that early developmental delay is a common ... -
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Impact of somato-cognitive coordination therapy on activities of daily living in a patient with Huntington’s disease.
Publication date: Dec 04, 2024 Huntington’s disease (HD) causes progressive neurodegeneration, impairing activities of daily ... -
New perspective on central nervous system disorders: focus on mass spectrometry imaging.
Publication date: Dec 05, 2024 An abnormally organized brain spatial network is linked to the ... -
HD Uncut: Days of Our Lives
Publication date: Dec 05, 2024 HD Uncut: Days of Our Lives Concepts Keywords Biosciences Beta ... -
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The pivotal role of histidine 976 in human histone deacetylase 4 for enzyme function and ligand recognition.
Publication date: Dec 01, 2024 Human histone deacetylase 4 (HDAC4) belongs to class IIa of ... -
CRISPR/Cas9-induced double-strand breaks in the huntingtin locus lead to CAG repeat contraction through DNA end resection and homology-mediated repair.
Publication date: Dec 03, 2024 The expansion of CAG/CTG repeats in functionally unrelated genes is ... -
Cognitive engagement may slow clinical progression and brain atrophy in Huntington’s disease.
Publication date: Dec 04, 2024 Lifelong cognitive engagement conveys benefits in Huntington’s disease (HD) and ... -
Beta-Blockers Tied to Delayed Huntington’s Disease Progression
Publication date: Dec 04, 2024 The premanifest Huntington’s group included 174 beta-blocker users (66% were ... -
The role of sirtuin 1 in ageing and neurodegenerative disease: A molecular perspective.
Publication date: Dec 01, 2024 Sirtuin 1 (SIRT1), an NAD+-dependent deacetylase, has emerged as a ... -
Iron homeostasis and neurodegeneration in the ageing brain: Insight into ferroptosis pathways.
Publication date: Dec 01, 2024 Ageing is a major risk factor for various chronic diseases ... -
Mitochondrial dysfunction as a therapeutic strategy for neurodegenerative diseases: Current insights and future directions.
Publication date: Dec 01, 2024 Neurodegenerative diseases, as common diseases in the elderly, tend to ... -
Evidence-Based Review on Symptomatic Management of Huntington’s Disease.
Publication date: Dec 02, 2024 Concepts Keywords Disease Based Disord Disease Evidence Disord Huntington Evidence ... -
Protective Effects of Antcin H Isolated from Antrodia cinnamomea Against Neuroinflammation in Huntington’s Disease via NLRP3 Inflammasome Inhibition.
Publication date: Dec 02, 2024 Huntington’s disease (HD) is an autosomal dominant neurodegenerative disorder caused ... -
Intrathecal baclofen pump for severe hypertonia in a patient with juvenile Huntington’s disease: illustrative case.
Publication date: Dec 02, 2024 While the symptoms of Huntington’s disease (HD) typically first appear ... -
Differential impact of optogenetic stimulation of direct and indirect pathways from dorsolateral and dorsomedial striatum on motor symptoms in Huntington’s disease mice.
Publication date: Jan 01, 2025 The alterations in the basal ganglia circuitry are core pathological ... -
Novartis wagers billions of dollars on PTC Huntington’s drug
Publication date: Dec 03, 2024 Research indicates this protein, which is often concentrated in the ...